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首页 > 【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例

【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例

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【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例 子宫圆韧带肌瘤伴左卵巢肌瘤1例 3[ ?????B??]1002-0179(2007)04-0899-01 ?????-???e???I?t?????????I1?? ????,???R?? 3 ,?l?f???? (?????l???????.???/????????,?????3??p?610041) p?p?[?b???-????]R737131;R737133p?p?p?[???d?7???[]E p?p????2,48??,G3P1 +2 ,???????t...
【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例
【doc】子宫圆韧带肌瘤伴左卵巢肌瘤1例 子宫圆韧带肌瘤伴左卵巢肌瘤1例 3[ ?????B??]1002-0179(2007)04-0899-01 ?????-???e???I?t?????????I1?? ????,???R?? 3 ,?l?f???? (?????l???????.???/????????,?????3??p?610041) p?p?[?b???-????]R737131;R737133p?p?p?[???d?7???[]E p?p????2,48??,G3P1 +2 ,???????t?9???g?? ??2 + ?9??2006??9?927??????p]???2??2006 ??6?9???6?S?????????4??????,???[???l?? ??,???9???g?k?C,?t?(?9???g?????????? ??8?o,?????B???v??,B?????k???Y???k?? ?l????,?????kq:???Y???k????qU,???????? ????(?????,??)?6,?????G??p]3????,?) ?????????h???????t?9???[??8?o,???b,?? ?;??????????,?????????????l????50?o?l ?R,???Y????????????4cm?l?R?2??,?/?? ?l??,?????????Y???k?(????p]B?????k???? ?????????Z???4???????V2??3?a?v????????, ???l????118cm,???R018cm,???Y???k 413cm??312cm??318cm?v??????(???P???e ?B?Z???4???I)p]???I?7????CA125:918U?? mL -1 ;CA19-9:218U??mL -1 p]???????l?g?? ?g012g???(????,q12h,?????;014g???(?? ??q12h,????????5?o?6,?)???????O??,?? ?2???K???????n????p] ?????????B?t?????????R,?t???w,?? ?????l,3???????(?????R??????2cm?l?R, ???? + 2?9???l?R,???Y???k??????4cm?l ?R????,?/???l??p]?????????n???????6, ??2006??9?929?????????????np]?n?b??: ????????????,????2 + ?9???l?R,???????? ????p[????p[?6???(?C?a?Z???4?????????? ?I,??????018??3cm,??????????,?????? ?C?0?D????????p]?????-???e??????2cm?0 ???l???3????4cm??4cm??5cm???I,?V??, ?(???????2??,???I?0?,???????J?-???ep] ???????l?R???J,????,?V??,?????????a ???6?S?]?Jp]???????a???6?S?]?J,?????? ?????l??????118cm,???(?2??????p]?n?b ?7??????p[???Y????????????p]?n?6?????? ?g?q?y?g???????(????????4?o?6,???9?? ??p]???-????:???????????I?t???l,???- ???e???I?t???l,?????????????????Ip] ????:???????I???g?V?P???e?????? ?2?;??,?V?????2???k?;??p]?????-???e?? ??????????????????,?;???4?????I???? ??,???????????????????l?t?7????p]???? ?-???e?D?(???????3?-,???(?????qp[???? ?q????,?(???g???I?????%p]?(???2???k?? ?????????I?n?????????????%???????????? ???????B?D?(???????????????????ep]?(?? ?????k???????I?6?????q???C?(??,?J?9?? ???????Ip] ?v???D?????8??,?????-???e???I???? ???g?V?????????B?B??p]???g?V??????????, ?????6?Z???4???????I?????????I???D;?? ?g?V?????B????,?G???????k????????p[?? ?l????????p[?]???I??p]???????I?n???G?R ??,?B?????k?????I??p]?q?????????????? B?????V???????????????k??,???????H?? ???V?n???????J??B???????B,?????????? ???????l?V,???D?n???l????,????CT?B MRI [1] p] ?????)???????2?(?6?S????,???6?S?? ??p[?9???O??,?B?2???????l,?l?V?,?6?? ?????n????p]???n???l????,???-???e???I, ?????n?k?/,?F???7?????I???2?????l???? ????,?n?6?????B???B?S??p] ???1???d [1]MichelP,ViolaD.Abdomino-pelvic leiomyomaoftheroundligament:contribu2 tionofcomputedtomographyandmagnetic resonanceimaging[J].JGynecolObstet BiolReport(Paris),2003,32(6):571 -457. (?u?X???g:2006-11-28) [?????B??]1002-0179(2007)04-0899-01 Laurence-Moon-Biedl???9??2?? ????,???n?? (?????l???????/?????-????,?????3??p?610041) p?p?[?b???-????]R59611p?p?p?[???d?7???[]E p?p?????1,???l,17??,???g?????(???? ????????,?3?3????????????,?t?:??,?C ??????p[???9??p]???27???)??,???k???? ?R???(????,?????,?)?8???8???????????8 ????p]????:?????l????,????140cmp[?? ??68kgp[?????7??34169,????90cmp[???? 100cmp[??/????????019p]?????????????? ??,???4?]???p??,?a???]?J???q???%p]?- ?J,?H???R,?/????,????,????p]???X?a ????,?B?t???C,???t??p[????p]???? (??)???7(??)p[????????????p]?H???? ??:?????????????q???lp]???2?u???????? ????,????????p]??????????:?????%?? 6172mmol/L,?3?62?R??13121mmol/L;?% ?Z?????q????47160mU/L,?3?62?R?? 149190mU/Lp]LH3125IU/L,E211134ng/L, P01161?g/L,FSHp[PRLp[T?????Jp]TSH 21174mU/L,FT3p[FT4???Jp]GnRH?????? ??:?V????LH1169IU/L,?V???615?-?? 22136IU/Lp[30?-??23161IU/Lp[60?-?? 18194IU/Lp[120?-??11156IU/Lp]?%???V?? ???????????Jp]?????????????]?J(?J?? 46XX)p]????p[??????:I?????????p[????, ??????p[?7????????p]?????C??(??)?? ??,?????????.5?????b???-??p]I??????? ?????????-?????????C?a???9p]B???S?k?? ?????R,?????Y???a???]?Jp] ????,?)?????2??????,??,?(?? ??(??)???7(??)p[????????????p[???q ?l??????????????,?Z???????J,?(?9?? (???I?9???h,?????;),???q9?a?9p] ????:Laurence-Moon-Biedl???9???? ?,???q?l????????-?C?7(??)????-?l?? ???,?????9??,?vLaurence??Moon??1866?? ????????,?.?B??20????Biedl???????t?? ??????????????????p]?????k??,?B?????d ???????(300????[1,2] ,?;????????10?? ??[3] p]?.???k?J?????????l???q?l????,?? 50%?????(??????,?????,?6,?????k?4?c ?;???o?l?????k???%??p]?/???t???????k?? ??p[???????4p[?l?????????,??p[???????? ?q???lp[?C?7(??)?B???7(??)????p]?V ?t???C?J?O???)?????????????-?k????:I? ??????:???V?)??5?a???.?t??????;I??, ??????:?k?;1??2?a???.?t??????;I????D ??(?b??)??:???(1??2?a???.?t??????; I???(?,)??????:?k?;?????????q???l, ?????????H???]?J;I????l??????:??5?a ???.?t???????B???t?????????o?l?]?J?B?? ?q?l????p]???B,?????????????C?????o?l ?]?J???g???????G??,???l?????q???l???q ????,?y????p[???)?????.?,???n??p]?;?? ?????(???X???????R?1????????p[?????q?? ??p]?????b???????(?)??5?a???.?t??????, ??????????,?P?8???9???(???t???y?????? ???????????X??,???V?????C?????h????p] ???%?ZLHp[E2p[P?t???????8GnRH?????? ?????J???k???V?4?c?;????p]?????2?????? ???(????p[?????????q???lp[?C??????,?k ?,??????p]?.??????,?P???s?l?C??,???? ?8?????????;??p]???????????????????(?. ???9???????-????,?P???????]?1??????, ?G?6Froehlich???9??p[?????l?C?7????p[ Prader-Willi???9??p[Alstrom???9??p[Kline2 felter???9????????p]?.???9???C???(?????? ????p]?.?????2?b?????,???(??????,???9 ?????X??p[???????q?%??,?/???????u????p[ ???k????????,???1???l???q????????,?8 ?????????,????????p] ???1???d [1]MohsinN,MarhubyH,MaimaniY,etal. Developmentofmorbidobesityaftertransplan2 tationinLaurenceMoonBiedlsyndrome[J]. TransplantProc,2003,35(7):2619. [2]ItayaS,IshimoriM,TakunoH,etal.A caseofLaurence-Moon-Biedlsyndromeas2 sociatedwithrenaltubularacidosisandkidney dysfunction[J].NipponNaikaGakkai Zasshi,1995,84(2):290-292. () [3]???C,???N??,???F??LM B???9????[]?/???P???g?? ??,,3(???))68 (?u?X???g35) 998?????/??2007,22(4)p?CN51-1356/R ??8 222 Japanese. .aurence-oon -iedl1J. 20001:. :2007-0-1
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