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【doc】肝肺综合征和门脉肺高压

2017-11-14 10页 doc 37KB 28阅读

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【doc】肝肺综合征和门脉肺高压【doc】肝肺综合征和门脉肺高压 肝肺综合征和门脉肺高压 !!????J!?t?Nj???N4?b ???????t???????o?????? ?7???2?1?? ???????t??(h??atopulmonarysyndrome?lHPs)?????o???? ??(portopulmonaryhypertensjon?lPPH)?O???C?????????<?c?? ????????????MJ???????n?????o?????????l???i?????*???p?? ?i?n?8?*?T?l...
【doc】肝肺综合征和门脉肺高压
【doc】肝肺综合征和门脉肺高压 肝肺综合征和门脉肺高压 !!????J!?t?Nj???N4?b ???????t???????o?????? ?7???2?1?? ???????t??(h??atopulmonarysyndrome?lHPs)?????o???? ??(portopulmonaryhypertensjon?lPPH)?O???C?????????<?c?? ????????????MJ???????n?????o?????????l???i?????*???p?? ?i?n?8?*?T?l???????????n???m?D???lMJ ???nHPS HPS?O?L?4???3???C???????????r???????7?????o?C?t ?J?[?P???????C?x???l???i?p?O?L?????C????M!?????x?????7 ?????C?x???x???y???o????MJ?????t??1956???LRydellHoff_ bauer?????????l1977??Kenned?nKnudSon????HPS??????MJ ???????l???r???????(????HPS?????b???*4?(??29?(MJ ???x?????J?[???7?OHPS???y?????A?l???n???x?????B ?J?[???x???????*??????PPH?m?lMJHPS???????????7?y?? ???x???J?[???7?l?????????????C?h?V???3?????????y???C?x ??MJ?o?????8?*?lHPS???(????????PPH?U???????????C?x ???i?????u???p????????MJ?FM!???????C?x??(Pa02<9?n33 kPa)????HPs?j??MJ HPs?w?????i???????)?z???o???????(MJ???r?????3?? ?u???n???C?x???u???????C???r?l????????ChildC?????(?o ?????????CMJ???????C???r??????Budd7Hchiari???t??M!?????? ?)?????o???????????3???C???r?????C?????x?????????o?? ?????(HPS???H???????l?????????m????HPS????MJHPS?? ?n?????l?????????????b?*2?l5?????H???8?*?l?????????* 41?(MJ (??)HPS???????*?????o?????7?y?????x???J?[???7?l ???o?????N???v???r???x???????l?????????z?C???????????7 ??????????MJ???????u?????????*???x???w?C???i?l?(?????< ????????a(TNFa)M!?x???7???C???????????C?)???????C?)?A ???8MJ?o?H?????n?l???????C?)?A?T????????HPs???????? ???????iMJ?????[?????C?)?A???????????????????o?C?h???? ????????MJ???)?l?????7?????w?C?J?[M!B???????7???????? ?????????nHPs???bMJ?????????(?????o???????????p??A ????B???????7???????w?l?????7?w?????3?B?x?????i?????o ?f?h?????iMJ?l?iHPs?????K???F?l???????????b?????C?) ?A?????lB???????7??????????????????MJ HPs?????N???h?v???O???????????x?????7???????o?? ?5?O???yMJ?5???x?????????????p???????v?????????????? ?x?????7?)?????1???????yMJ ???)?l?C???x?????????????u??M!???S???7???x?????7?? ??M!?????????o???????????o???h?VM!?????n?????x???C?3???? ???(?????5200032?p???m???C???????F???w?????)?? ??261?? ???????????? ??M!?5?H?r?x?V?????L?j??????M!???z???<?????n??HPs???? ?yMJ (??)HPS???z???????n?????L???N?????(???????C?? ???????l?5?????(?O?i?4?????????x?p?y?y???????[?????? ???l??????M!???[????M!?????C?*?CM!???????[M!?????a???????? ???x?????7(?1????)??MJ?????C???[?????OHPs???[?????? ??????MJ???????????N???n?8?I?C????MJ ???C?x???O????HPs??????????MJ?????C?*?C???????? ?[?O?N???????????C????MJ?????C?*?C?O?a???(?L???????v ?*?????????lPa02????10?(MJ???????[?O?a???(?L???????v ?*????????????????M!????M!?H???????l?l???m?????????!???p ???????v??MJ???????L?????u???x?V?????????l?5?H???x?V?? ???L?j?????l?????h?V?????7?y?????????[?????????l?????? ?????o???C?t?????l?*?C?i?????????M?e??MJ?x???l???i???? ?????????h?T???x?H?h??MJ???[lOO?(???C?????????x?H?h?? ?????M???????s???h?V???u??MJ ???????????????????C?)???3???????????l???m?O???? HPS??????????MJ ?x?o???i???C?????????C?x???????(?lHPs???????????o ?????x?????7??????MJ?????????*???????????O?????????x?? ???7?????????C?????????o????MJ???[?i?????????*???????? ????99mTc?a???????t??????(997RTcMMA)????????MJ?????? ?iHPS?????h?V?l?i?x???????4?G???M???n3??6?c???????b ???l?????i?????W?8??MJ?????????W???????????8?????*???i ???????s???h?V?l???????????????i?????W?????????m?l?*?h ?????h?V???????h?VMJ???????????????*???????????O?????y ??????????MJ?5?[?????u?l?????*20??m997RTcMMA???????? ?????i??????MJ???????s???h?V?????i?)?(?????x?????7?? ???i???????????????C?s?)?(?8?r????????997RTc?????t???? ??MJ???????O???????i???????????MHPS?h?V?u??MJ?????? ???????????M???C?x???u???l?A???????O?k?????????m???*?? ??????MJ?z?C?????m??????????HPSMJ ???????*???x???7???O?O???????x???v?????????????a ??MJ???L?????O?????6?<?C???????O?l?m???*HPS???[???? ??????MJ?????[?C???????????(?l???x???7???O?????*?THPs ???C?x???????e???x?????C?x???l?????*HPs???(?o???)?? ????????????????MJ (?o)HPS??????????????HPS???????C?5?*?O?!?C?? ???l?5????????????MJ???N?i?????????????x?p?l???r???G?l ?????b?????z?g???i?????l?????*?????O?!????MJ?[?C?????? ???????C?x???l???????????3?????i???????s???h?V?????(?l 262 ?? ?[?C???????????????C?x??MJ ???h???p???lHPs???h?????????(???????)???????????? ???b?h???????x?????7???????????l???????C?5?????(?????? ?m?????M?h??????????MJ???C?)?A?z???????????*???c???i ???????s?l?????????????5?c???[?????iMJ??L?????i??(???C ?)?A?t?y??????)?????m???k?????????4MJ???o???4???G???? 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